Cutaneous small vessel vasculitis

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Revision as of 18:33, 17 July 2024 by Nikolas (talk | contribs) (Created page with "<section begin="dermatology" />* Small vessel vasculitides with cutaneous involvement * Most cases are idiopathic * Types ** Immune complex mediated vasculitides *** Cryoglobulinaemic vasculitis *** <abbr>IgA</abbr> vasculitis = Henoch Schönlein purpura *** Urticarial vasculitis ** ANCA-associated vasculitides *** Granulomatosis with polyangiitis *** Eosinophilic granulomatosis with polyangiitis * Common clinical features ** Palpable purpuras ** Erythematous papules **...")
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  • Small vessel vasculitides with cutaneous involvement
  • Most cases are idiopathic
  • Types
    • Immune complex mediated vasculitides
      • Cryoglobulinaemic vasculitis
      • IgA vasculitis = Henoch Schönlein purpura
      • Urticarial vasculitis
    • ANCA-associated vasculitides
      • Granulomatosis with polyangiitis
      • Eosinophilic granulomatosis with polyangiitis
  • Common clinical features
    • Palpable purpuras
    • Erythematous papules
    • Urticaria
    • Systemic symptoms
      • Fever
      • Myalgia
      • Arthralgia
      • Renal disease
  • Prognosis
    • 90% spontaneously resolve within months
    • 10% become chronic or recurrent