Ebstein anomaly: Difference between revisions
(Created page with "<section end="radiology" />'''Ebstein anomaly''' is a rare form of cyanotic congenital heart disease characterised by a downwards displacement of the septal and posterior leaflets of the tricuspid valve into the right ventricle. This displaces the "border" between the right atrium and right ventricle inferiorly, making the right atrium larger and right ventricle smaller, a process called atrialisation.<section end="radiology" /> Depending on the exact pathology and...") |
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Revision as of 10:41, 4 December 2023
Ebstein anomaly is a rare form of cyanotic congenital heart disease characterised by a downwards displacement of the septal and posterior leaflets of the tricuspid valve into the right ventricle. This displaces the "border" between the right atrium and right ventricle inferiorly, making the right atrium larger and right ventricle smaller, a process called atrialisation.
Depending on the exact pathology and any concomitant heart defects, the clinical features can vary significantly.
Diagnosis and evaluation
Echocardiography confirms the diagnosis. Chest radiography shows a box-shaped heart.